autores Ana João Gomes Rodrigues de Voer, G. Bent, P. van der van Bent, P. Rodrigues, A.J.G. Ommen, G.-J. B. van van Ommen, G.-J.B. Peters, D.J.M. Taschner, P.E.M.
palavras-chave Alleles Animals Caenorhabditis elegans Carbohydrate metabolism Cosmids DNA Primers Disease models, Animal Female Gene deletion Genes, Reporter Green fluorescent proteins Lysosomes Male Membrane glycoproteins Microscopy, Electron Microscopy, Fluorescence Models, Genetic Models, Statistical Molecular chaperones Mutation Mutation, Missense Neurodegenerative diseases Neuronal Ceroid-Lipofuscinoses Neurons Phenotype Progeria Promoter regions, Genetic Recombinant fusion proteins Time factors Transgenes